Surgical management of progressive pulmonary venous obstruction after repair of total anomalous pulmonary venous connection

Background: The occurrence of a progressive pulmonary venous obstruction af ter the repair of the total anomalous pulmonary venous connection is a seve re complication. Objectives: The objectives of this study were to retrospec tively review the patients with this condition and to report our experience with a new surgical technique with a sutureless in situ pericardium repair , Methods: Of 178 patients who underwent correction of total anomalous pulm onary venous connection, 16 patients (9%) experienced the development of a progressive pulmonary venous obstruction in a median interval of 4 months ( 5 weeks-12 years). Three patients had isolated anastomotic stenosis, 4 pati ents had isolated pulmonary venous ostial stenosis, and 9 patients had both . Pulmonary venous obstruction was bilateral in 7 patients. The surgical pr ocedures used at reoperation included 8 patch enlargements, 5 ostial endart erectomies, 1 intraoperative stenting, and 7 sutureless in situ pericardium repairs. Results: There were 4 deaths after reoperation (4 of 15 patients; 27%). The only significant mortality risk factor was the bilateral locatio n of the pulmonary venous obstruction (P = .045). In patients with isolated anastomotic stenosis or with only 1 pulmonary venous ostial stenosis (n = 5), there was no death, except the patient presenting with a single ventric le, In patients with 2 or more pulmonary venous ostial stenoses (n = 10), t here were 3 deaths; 5 of the 7 survivors were successfully treated with the in situ pericardial technique, with normalized pulmonary artery pressure a t a mean follow-up of 26 months. Conclusion: Progressive pulmonary venous s tenosis after repair of total anomalous pulmonary venous connection remains a severe complication when bilateral. The sutureless in situ pericardial r epair offers a satisfactory solution, particularly on the right side.