Fibrous dysplasia with intramuscular myxoma (Mazabraud's syndrome) - Report of a case and review of the literature

Authors
Thomachot, B Daumen-Legre, V Pham, T Acquaviva, PC Lafforgue, P
Citation
B. Thomachot et al., Fibrous dysplasia with intramuscular myxoma (Mazabraud's syndrome) - Report of a case and review of the literature, REV RHUM, 66(3), 1999, pp. 180-183
Citations number
15
Categorie Soggetti
Rheumatology
Journal title
REVUE DU RHUMATISME
ISSN journal
11698446 → ACNP
Volume
66
Issue
3
Year of publication
1999
Pages
180 - 183
Database
ISI
SICI code
1169-8446(199903)66:3<180:FDWIM(>2.0.ZU;2-V
Abstract
About 30 cases of fibrous dysplasia associated with one or more myxomas (Ma zabraud's syndrome) have been reported since 1926. We report a new case in a woman with polyostotic fibrous dysplasia and a myxoma in the left femoral muscle. She also had a history of precocious sexual development and cafe a n lait spots, two manifestations whose association with polyostotic fibrous dysplasia defines McCune-Albright syndrome.