We herein present a patient with lipomatosis of the ileum including di
verticulosis and volvulus. The patient presented with abdominal pain a
nd vomiting. Preoperatively, we diagnosed lipomatosis with volvulus of
the ileum based on the findings of abdominal ultrasonography (US) and
computed tomography (CT), During surgery, the dilated ileum had rotat
ed 720 degrees C counterclockwise, and was found to contain lipomatosi
s and multiple diverticula. Although lipomatosis of the small bowel is
extremely rare, if does show characteristic US and CT findings, thus
making a preoperative diagnosis possible if this disease is included i
n the differential diagnosis.