RECURRENT PSEUDOMONAS BRONCHOPNEUMONIA AND OTHER SYMPTOMS AS IN CYSTIC-FIBROSIS IN A CHILD WITH TYPE-I PSEUDOHYPOALDOSTERONISM

We report a child with multiple target organ pseudohypoaldosteronism t ype 1 with frequent recurrent pulmonary infections caused by Pseudomon as aeruginosa and Pasteurella multocida and high levels of chloride in sweat, urine and nasal secretion. Repetitive faecal chymotrypsin samp les have all shown pathological values in spite of no other sign of ex ocrine pancreas dysfunction. The similarities with cystic fibrosis and the importance of the salt content in bronchial fluid are discussed.