OPTIC-NERVE HEAD SWELLING IN THE HADJU-CHENEY-SYNDROME

The Hadju-Cheney syndrome is one of the idiopathic acro osteolyses. As sociated neurologic abnormalities are often a result of progressive ba silar invagination. A 48-year-old man with the Hadju-Cheney syndrome d eveloped progressive bilateral visual loss. On examination, he had hyp eropia, choroidal folds, optic nerve head swelling, and mild optic neu ropathy. Computed tomographic scans showed massive enlargement of both intraorbital optic nerve sheaths. Improvement occurred after optic ne rve sheath fenestration. Visual loss due to optic nerve meningocele ca n occur in the Hadju-Cheney syndrome. Optic nerve sheath fenestration can result in visual improvement. It is unclear whether the occurrence of optic nerve meningocele is causally or fortuitously related to the Hadju-Cheney syndrome.