OPTIC NEUROPATHY IN MCCUNE-ALBRIGHT-SYNDROME - AN INDICATION FOR AGGRESSIVE TREATMENT

McCune-Albright syndrome consists of the tried polyostotic fibrous dys plasia, cafe-au-lait spots and autonomous hyperfunction of one or more endocrine systems. The most frequent neurological complication of cra niofacial fibrous dysplasia is visual loss. We describe a 17-y-old boy with McCune-Albright syndrome and acute loss of vision in the left ey e caused by encroachment of the left optic nerve by fibrous dysplastic lesions. Neurosurgical intervention improved left eye vision. Aggress ive intervention is indicated in cases of acute visual loss in patient s with craniofacial fibrous dysplasia. This is supported by a review o f other reported cases.