SCLEROATROPHIC SYNDROME OF HURIEZ IN AN INFANT

We present a 3-year-old boy with scleroatrophic syndrome of Huriez, a rare autosomal dominant condition with only seven affected families wo rldwide. Although assumed to occur from birth, an evolving case has no t previously been documented. Infants do not possess the focal areas o f keratoderma on the palms or soles; these develop in adult life. Of p articular interest is the high incidence of squamous cell carcinomas t hat arise from the scleroatrophic skin.