KERATITIS, ICHTHYOSIS, AND DEAFNESS (KID) SYNDROME IN HALF SIBS

The keratitis, ichthyosis, and deafness (KID) syndrome is a rare conge nital disorder of the ectoderm characterized by diffuse hyperkeratotic erythroderma, keratitis with neovascularization of the cornea, and se vere neurosensory hearing loss, A familiar occurrence of this syndrome has been mentioned in four reports including three of vertical transm ission and one of two affected sisters born from consanguineous, unaff ected parents. We report far the first time a familial case of KID syn drome in two half siblings born to the same unaffected mother, This ne w observation allows us to propose various hypotheses about its mode o f inheritance.