DOUBLE-OUTLET RIGHT VENTRICLE WITH SUBAOR TIC OBSTRUCTION CREATED BY HYPERTROPHY OF A PARIETAL BAND - ECHOCARDIOGRAPHIC CASE-REPORT

The authors report the case of an 18 month old infant with double-outl et right ventricle and subaortic ventricular septal defect with severe subaortic obstruction. Echocardiography showed the subaortic obstruct ion to be due to severe hypertrophy of the parietal band which grew up wards to the aortic annulus. A peak instantaneous Doppler gradient of 72 mmHg was recorded between the right ventricle and the aorta. The hy pertrophy of the band was secondary to pulmonary artery banding perfor med in the neonatal period at the same time as cure of an isthmic coar ctation of the aorta. Surgical exploration confirmed the echocardiogra phic findings a circular subaortic muscular stenosis related to hypert rophy of the parietal band. Resection of this band liberated the left ventricular outflow tract and made possible a tunellisation procedure between the left ventricle and the aorta. Postoperative Doppler echoca rdiography showed the absence of subaortic stenosis.