SMALL INFARCTIONS OF COCHLEAR, RETINAL AN D ENCEPHALIC TISSUE SYNDROMA OF THE YOUNG-PEOPLE, OR SICRET SYNDROME OR SUSACS-SYNDROME

A 22-year-old-lady presented with multiple occlusions of the branches of the central retinal artery, accompanied by neuroencephalic disorder s and deafness. This triad is known as SICRET Syndrome (Small Infarcti on of Cochlear, Retinal and Encephalic Tissue). This rare syndrome, as well referred to as Susac syndrome, affects only the women and the th ree tissues mentioned above : eye, ear, brain. The course was characte rised by a series of partially regressive evolutive steps. A remission had been obtained since two years with immuno-supressor and anti-coag ulant therapy. The neuro-encephalic and cochlear disorder regressed in contrast to the severe sequel on the right eye.