A 10-year-old girl underwent radical decompression of a right temporal
tumour extending to the insular cortex which proved to be a different
iated ganglioglioma. One year later, she presented with a bleeding rig
ht frontal tumour extending to the insula, the histology of which show
ed it to be the anaplastic variant of ganglioglioma. She underwent pos
toperative radiotherapy but died 6 months after the second operation.
Anaplastic ganglioglioma is a rare variant of ganglioglioma and progre
ssion of the latter to anaplastic ganglioglioma is an extremely rare o
ccurrence. The literature regarding ganglioglioma is reviewed.