Objective/Hypothesis: Cases of cholesteatoma in pediatric patients wer
e reviewed to determine which factors influence the outcome of surgica
l treatment. Cholesteatoma is considered a more aggressive disease in
children than in adults. The outcomes of intact canal wall (ICW) masto
idectomy and canal wall down (CWD) mastoidectomy were assessed, as com
parisons of different surgical technique. Study Design: A retrospectiv
e analysis of all cases of pediatric cholesteatoma treated at a single
institution by the senior author (P.R.L.) over a period of 11 years w
as conducted. Methods: Patient information was collected hom an otolog
y database, patient records, and audiology files, Results: Sixty six p
atients, aged 10 months to 18 years, were treated and followed for an
average of 37.7 months (range 12.2 months to 12. 5 y), ICW mastoidecto
my with tympanoplasty was the primary surgical treatment in 41 patient
s, Nineteen percent had residual disease at a planned second stage sur
gery and 22% developed recurrent cholesteatoma for a total recidivism
rate of 41%, A SRT of less than 30 dB HL was achieved in 75% of these
patients. Seventeen patients underwent CWD mastoidectomy with tympanop
lasty initially. Two patients (12%) had residual cholesteatoma found a
t a planned second state procedure, and no recurrent cholesteatoma was
encountered Seventy-two percent maintained a SRT of less than 30 dB H
L, Conclusions: These results support the continued use of ICW mastoid
ectomy with tympanoplasty for pediatric cholesteatoma. if planned seco
nd stage surgery is necessary, the long-term results of an ear with us
eful hearing and few problems with chronic medical care are gratifying
. For reasons of anatomy or in an only hearing ear, CWD mastoidectomy
with tympanoplasty provides a safe ear and good hearing results. Masto
id cavity care must be maintained indefinitely in many cases.