PERSISTENCE OF THE INTESTINAL DEFECT IN ABETALIPOPROTEINEMIA AFTER LIVER-TRANSPLANTATION

Authors
BRAEGGER CP BELLI DC MENTHA G STEINMANN B
Citation
Cp. Braegger et al., PERSISTENCE OF THE INTESTINAL DEFECT IN ABETALIPOPROTEINEMIA AFTER LIVER-TRANSPLANTATION, European journal of pediatrics, 157(7), 1998, pp. 576-578
Citations number
8
Categorie Soggetti
Pediatrics
Journal title
European journal of pediatrics → ACNP
ISSN journal
03406199
Volume
157
Issue
7
Year of publication
1998
Pages
576 - 578
Database
ISI
SICI code
0340-6199(1998)157:7<576:POTIDI>2.0.ZU;2-L
Abstract
A 16-year-old girl is described with abetalipoproteinaemia who underwe nt liver transplantation for hepatic cirrhosis. After this procedure h er serum lipoprotein profile was corrected, however, fat malabsorption and steatorrhea persisted because the primary defect, a mutant micros omal triglyceride-transfer protein, remains expressed in the intestine .