Congenital microgastria is an uncommon result of impairment of normal
foregut development. To date, only 39 cases have been described in the
literature. We report a boy born with microgastria and bilateral hypo
plastic kidneys who had feeding problems, resulting in failure to thri
ve and growth retardation. After a short period of conservative manage
ment, he was operated upon at the age of 11 months. A Hunt-Lawrence po
uch was created, leading to toleration of increasing amounts of oral f
eeding. Although his feeding problems have decreased, his height and w
eight are below normal (<10th percentile). The embryology, clinical pr
esentation, procedures, associated and management are bryology, diagno
stic anomalies, discussed.