Familial idiopathic nephrotic syndrome is rare. Only about 3% of patie
nts have affected siblings. The association of familial nephrotic synd
rome with congenital abnormalities is even more uncommon. To our knowl
edge this is the first report of the association of steroid-sensitive
nephrotic syndrome and postaxial hexadactyly in two brothers born to c
onsanguineous parents.