In retinitis pigmentosa patients the effect of cystoid macular edema o
n colour vision was studied. The occurrence of cystoid macular edema d
ecreases with increasing colour vision defect. The mutual proportion o
f the main types of colour vision defects remains stable until visual
acuity has dropped to 0.5; at lower VA levels the number of red-green
defects increases. Neither the finding of a blue-yellow colour vision
defect in FM 100 Hue testing nor the appearance of anomaloscopic pseud
oprotanomaly is influenced by cystoid macular edema. The authors concl
ude that cystoid macular edema in retinitis pigmentosa patients mainly
affects visual acuity and not colour vision. They also noted a famili
al occurrence of cystoid macular edema.