CORONARY ARTERIOVENOUS-MALFORMATIONS IN A PATIENT WITH HEREDITARY HEMORRHAGIC TELANGIECTASIA - A CASE-REPORT

Hereditary hemorrhagic telangiectasia (Osler-Weber Rendu) disease is c haracterized by cutaneous, mucosal, and visceral vascular anomalies. T wo patients were previously described with coronary artery aneurysms ( ectasia) associated with this disease. This report describes a patient with Osler-Weber-Rendu disease in whom multiple coronary arteriovenou s malformations were identified during coronary angiography. The patie nt presented with anginal chest pain resulting from severe anemia. Upp er gastrointestinal endoscopy revealed multiple;angiodysplastic lesion s throughout the esophagus and stomach.