CHONDROSARCOMA IN NASAL FOSSAE AND MAFFUCCIS-SYNDROME

Citation
F. Retornaz et al., CHONDROSARCOMA IN NASAL FOSSAE AND MAFFUCCIS-SYNDROME, La Revue de medecine interne, 19(7), 1998, pp. 501-505
Citations number
12
Categorie Soggetti
Medicine, General & Internal
ISSN journal
02488663
Volume
19
Issue
7
Year of publication
1998
Pages
501 - 505
Database
ISI
SICI code
0248-8663(1998)19:7<501:CINFAM>2.0.ZU;2-H
Abstract
Introduction. - Maffucci's syndrome is a congenital non-hereditary dis ease very similar to Ollier's disease and associates multiple cutaneou s hemangiomas, dyschondroplasia and often enchondromas. Exegesis. - We report a unique case involving synchronous localization of chondrosar coma in nasal fossae and anterior chest wall, disclosing Maffucci's sy ndrome. Conclusion. - Atypical chondrosarcoma localization must lend t o further investigation of potential multiple enchondromatosis. (C) 19 98, Elsevier, Paris.