ASSOCIATION OF PULMONARY-ARTERY ANEURYSM, RIGHT HEART THROMBOSES AND ANTIPHOSPHOLIPID ANTIBODIES IN BEHCETS-DISEASE - A CASE-REPORT

Introduction. - Cardiac thromboses are unusual in the course of Behcet 's disease and are frequently associated with endomyocardial fibrosis of the right heart. Vascular pulmonary involvement with either pulmona ry aneurysm or parenchyma alterations is also often observed. However, pathogenesis of thromboses occurring in the course of Behcet's diseas e is still unclear. Case report. - The authors report the case of a 28 -year-old man who presented with Behcet's disease accompanied by pulmo nary aneurysm, multiple thrombi of the right heart and antiphospholipi d antibodies. Conclusion. - The choice of therapeutical strategies for curative treatment of this association as well as the interpretation of the role of antiphospholipid antibodies in this polyvascular diseas e raises questions. (C) 1998, Elsevier, Paris.