SIRENOMELIA - PRENATAL-DIAGNOSIS AND MANAGEMENT OF AN UNCOMMON MALFORMATION

Citation
W. Heyl et al., SIRENOMELIA - PRENATAL-DIAGNOSIS AND MANAGEMENT OF AN UNCOMMON MALFORMATION, Zeitschrift fur Geburtshilfe und Perinatologie, 202(3), 1998, pp. 121-126
Citations number
30
Categorie Soggetti
Pediatrics,"Obsetric & Gynecology
ISSN journal
09482393
Volume
202
Issue
3
Year of publication
1998
Pages
121 - 126
Database
ISI
SICI code
0948-2393(1998)202:3<121:S-PAMO>2.0.ZU;2-S
Abstract
Sirenomelia or the mermaid syndrome is a rare birth defect, often comb ined with severe malformations of the urogenital system and the lower gastrointestinal tract. The incidence is about one case in 60 000. Ult rasound can be very important in early detection of this deformity. Be cause of the high incidence of oligohydramnios amnioninfusion could be helpfull. Also a magnetic resonance radiographia in the prenatal peri od could be performed. We report three cases of sirenomelia and in add ition the literature is reviewed and discussed.