Laryngeal rhabdomyosarcoma is a rare disease. Only nine of these tumou
rs have been adequately described in world literature in the adult pop
ulation. Adult patients with laryngeal rhabdomyosarcoma often present
at a later stage than other laryngeal rumours, including squamous cell
carcinoma. Diagnosis is made by identification of cross-striations hi
stochemically or cytoplasmic myoglobin by immunohistological methods.
We present a 66-year-old woman with pleomorphic rhabdomyosarcoma of he
r larynx. This is the first female in the adult age group to be presen
ted. Surgical treatment with adjuvant radiotherapy is currently the tr
eatment of choice for this disease. We provide a review of the literat
ure on laryngeal rhabdomyosarcoma, including presentation, pathology a
nd management of this rare disease.