RAPIDLY PROGREDIENT SCOLIOSIS ASSOCIATED WITH MULTICORE DISEASE

Multicore disease is a rare congenital myopathy that normally stops or makes slow progress. It starts with delayed motor development and fre quent falls. Especially the proximal muscles are invovled. Other sympt oms include contractures of joints, clubfoot, high arched palate, ches t deformities, involvement of eye-muscle, cardiac abnormalities, hyper lordosis and scoliosis that normally does not require surgery. We repo rt a rare case of advanced scoliosis in multicore disease requiring op erative treatment in a 15-year-old girl. In this case the scoliosis to ok a rapidly progredient course in puberty close to the end of skeleta l growth. A dorsal spondylodesis with USS instrumentation from T9 to L 3 was performed. A significant reduction of the scoliosis was obtained . Scoliosis in multicore disease may take a rapidly progredient course . Frequent checks will lead to the initiation of surgical treatment in time.