CONGENITAL UNILATERAL SPECKLED LENTIGINOUS BLUE NEVI WITH ASYMMETRIC SPINAL MUSCULAR-ATROPHY

We describe a 30-year-old man presenting with congenital widespread un ilateral hyperpigmented areas on the right side of the face and limbs that were studded with multiple blue nevi. There was nevus of Ota-like scleral involvement of the right eye. Histologic examination showed c ommon blue nevi, one in association with lentigo. For this unusual typ e of dermal melanocytosis we propose the term, congenital unilateral s peckled lentiginous blue nevi. In addition, the patient had monomelic spinal muscular atrophy of his right shoulder girdle and arm.