INHERITED RETINAL TELANGIECTASIA WITH GLIAL PROLIFERATION

We describe five patients from a family of Pakistani origin with inher ited retinal telangiectasia and glial proliferation. Characteristics o f this condition include: variable visual loss; peripapillary retinal telangiectasia with vascular incompetence on fluorescein angiography; glial proliferation; cystoid macular edema or altered macular pigment; retinal hemorrhage; and abnormal electroretinopathy. We discuss the s imilarities with and distinguishing features from other documented con ditions and the mode of inheritance.