We reviewed retrospectively the clinical and surgical data from 9 chil
dren with postoperative chylothorax secondary to cardiac surgery for c
ongenital heart disease seen over a 3 year period. Mean age was 26 mon
ths and 6 patients were female. The procedures performed were 2 Blaloc
k-Taussig shunts, 6 Bidirectional Glenn anastomoses and 1 modified Fon
tan procedure. Diagnosis of chylothorax was made by classical means. T
he overall incidence of chylothorax was 0.8%, with the relative incide
nces being 2.5% for Blalock-Taussig, 2.7% for Fontan, and 11.7% for th
e Glenn procedures. All patients were initially treated conservatively
with chest tube drainage and hypercaloric diet suplemented with mediu
m chain triglycerides. Parenteral nutrition was needed in 2 patients,
one because of sepsis and the other because of progressive malnourishm
ent. High output fistulas and long periods of drainage were noted afte
r cavo-pulmonary procedures. Up to 12% weight loss was observed in 6 p
atients, one patient was successfully treated of pneumonia and another
died of Pseudomonas aeruginosa sepsis. Two patients required chemical
pleurodesis because of unabated drainage, with the others being succe
ssfully treated conservatively. Chylothorax is a common complication a
fter bidirectional Glenn procedures, and is associated with considerab
le morbidity and mortality. Earlier operative intervention may be requ
ired in these patients. Pleurodesis is a simple, safe, and effective p
rocedure to stop chylous flow.