Echocardiographic examination, performed in an asymptomatic Ei year ol
d boy for a perimembranous ventricular septal defect (VSD), revealed a
6 x 6 mm tumor on the anterior leaflet of the mitral valve. Clinicall
y, it was diagnosed as a benign myxoma. Histopathologic diagnosis of t
he excised mitral valve turner was benign lipoma. The third case of mi
tral valve lipoma in the pediatric age group is reported along with a
review of the literature. Echocardiogram remains the most sensitive di
agnostic modality in the early detection of such neoplasms.