Although most cases of pilonidal sinus occur in the sacrococcygeal reg
ion, umbilical presentations can occur. Due to the risk of peritoneal
extension of inflammation from this lesion, the umbilical pilonidal si
nus should be treated more aggressively than its sacrococcygeal counte
rpart. Pilonidal sinus should therefore be included in the differentia
l diagnosis of umbilical nodules.