NEVUS COMEDONICUS SYNDROME - A NEW PEDIATRIC CASE

Nevus comedonicus (NC) is an uncommon developmental defect of the pilo sebaceous apparatus, The individual lesions are large comedones often arranged in groups or in a linear pattern. Nevus comedonicus syndrome (NCS) is a well-defined disorder within the large group of epidermal n evus syndromes. In patients suffering from NCS, the nevus is associate d with noncutaneous abnormalities including skeletal defects, cerebral anomalies, and cataracts. We report a 9-year-old boy with open comedo nes in a linear pattern localized to the right cheek, clinodactyly and polydactyly of the first right finger, bilateral syndactyly of the se cond and third toes, and some depigmented hairs since birth.