Fm. Akgur et al., A CASE OF SPLIT NOTOCHORD SYNDROME - PRESENCE OF DORSAL ENTERIC DIVERTICULUM ADJACENT TO THE DORSAL ENTERIC FISTULA, Journal of pediatric surgery, 33(8), 1998, pp. 1317-1319
Like umblical enteric remnants (eg, umblical sinus and omphalomesenter
ic fistula), enteric remnants can be seen on the dorsal aspect of the
body (dorsal enteric sinus, dorsal enteric fistula [DEF], dorsal enter
ic diverticulum) in conjunction with complete cleft of the vertebral c
olumn. Complete cleft of the vertebral column associated with gastroin
testinal tract and central nervous system anomalies is known as ''spli
t notochord syndrome'' (SNS). The authors present an unreported va ria
nt of SNS having do rsa I enteric diverticulum adjacent to the DEF. Th
e patient died 17 days after surgical repair. Copyright (C) 1998 by W.
B. Saunders Company.