A CASE OF SPLIT NOTOCHORD SYNDROME - PRESENCE OF DORSAL ENTERIC DIVERTICULUM ADJACENT TO THE DORSAL ENTERIC FISTULA

Like umblical enteric remnants (eg, umblical sinus and omphalomesenter ic fistula), enteric remnants can be seen on the dorsal aspect of the body (dorsal enteric sinus, dorsal enteric fistula [DEF], dorsal enter ic diverticulum) in conjunction with complete cleft of the vertebral c olumn. Complete cleft of the vertebral column associated with gastroin testinal tract and central nervous system anomalies is known as ''spli t notochord syndrome'' (SNS). The authors present an unreported va ria nt of SNS having do rsa I enteric diverticulum adjacent to the DEF. Th e patient died 17 days after surgical repair. Copyright (C) 1998 by W. B. Saunders Company.