FATTY-ACID BETA-OXIDATION DEFICIENCY MASQUERADING AS FULMINANT MYOCARDITIS

Authors
DELONLAYDEBENEY P FOURNET JC BONNET D
Citation
P. Delonlaydebeney et al., FATTY-ACID BETA-OXIDATION DEFICIENCY MASQUERADING AS FULMINANT MYOCARDITIS, International journal of cardiology, 65(3), 1998, pp. 287-289
Citations number
10
Categorie Soggetti
Cardiac & Cardiovascular System
Journal title
International journal of cardiology → ACNP
ISSN journal
01675273
Volume
65
Issue
3
Year of publication
1998
Pages
287 - 289
Database
ISI
SICI code
0167-5273(1998)65:3<287:FBDMAF>2.0.ZU;2-P
Abstract
We present a 9-month-old child presenting with acute cardiomyopathy an d fever following a viral illness. He was diagnosed to have acute myoc arditis, was proposed for an external hemodynamic assistance but died of ventricular tachycardia. Post-mortem data revealed a very-long-chai n acylcoenzyme A dehydrogenase deficiency. Our report raises awareness on the interest for preserving tissue samples and for performing a me tabolic screening in acute childhood cardiomyopathy. (C) 1998 Elsevier Science Ireland Ltd.