A. Zamir et al., IMMUNOPROLIFERATIVE SMALL-INTESTINAL DISEASE IN A 16-YEAR-OLD BOY PRESENTING AS SEVERE MALABSORPTION WITH EXCELLENT RESPONSE TO TETRACYCLINE TREATMENT, Journal of clinical gastroenterology, 27(1), 1998, pp. 85-89
Immunoproliferative small intestinal disease (IPSID) is a ran lympho-p
roliferative disorder of the upper small intestine. It is considered a
special form of MALT lymphoma with propensity to malignant transforma
tion. This disorder is rare in pediatric literature. We report a case
of IPSID in a 16-year-old boy with low-grade malignant transformation,
presenting as severe malnutrition and a possible association with Hel
icobactor pylori. The patient responded well to an extended treatment
with tetracycline and eradication of H. pylori.