A follow-up study of colour vision in two patients with gyrate atrophy
was performed. Gyrate atrophy was diagnosed in the first patient at t
he age of 17 years. Her colour vision was first tested at the age of 2
5 years; at the follow-up examination 7 years later, she correctly int
erpreted the Standard Pseudoisochromatic Plates part 2, however, with
one mistake due to lens opacity. In the Farnsworth-Munsell 100 hue tes
t and in the Color Vision Meter 712 (CVM) anomaloscope, the results we
re within normal ranges. In the second patient, gyrate atrophy was dia
gnosed at the age of 4 years. At the ages of 4 and 5 years, he correct
ly interpreted the Ishihara, AO H-R-R, and Lanthony Tritan Album plate
s as well as the City University test. At the ages of 6, 7, and 8 year
s, he correctly interpreted the plate tests, the Farnsworth Panel D 15
, and Lanthony's Desaturated Panel. The CVM anomaloscope results were
normal. (C) 1998 Elsevier Science Ltd. All rights reserved.