DYSKERATOSIS-CONGENITA ASSOCIATED WITH HODGKINS-DISEASE

Dyskeratosis congenita is a rare, hereditary, multisystem disorder cha racterized by mucocutaneous changes, pancytopenia and increased incide nce of malignancy. Different types of neoplasia have been reported in association with dyskeratosis congenita. We present a second case asso ciated with Hodgkin's disease. Delayed appearance of dermatological si gns and association with chronic hepatitis B are other unusual feature s of this case.