DIFFUSE SPLENIC AND VISCERAL HEMANGIOMAS COMPLICATED BY CHRONIC CONSUMPTION COAGULOPATHY

The case of a 7-year-old girl with a 2 year history of easy bruising a ssociated with thrombocytopenia is reported. On admission she presente d with ecchymoses, abdominal distention and splenomegaly. Hemostasis i nvestigation revealed a consumption coagulopathy. Several radiological studies failed to confirm the diagnosis of diffuse splenic and viscer al hemangiomatosis, which was eventually estasblished by an explorativ e laparotomy. Platelet count and the other coagulation abnormalities p rogressively returned to normal after splenectomy, although the remain ing hemangiomas were extensive.