We describe two Japanese girls with discoid lupus erythematosus (DLE)
in whom the condition showed a linear configuration, following the lin
es of Blaschko. The clinical appearance was unusual but histological e
xamination established the diagnosis;. After reviewing the previous re
ports, we found that in six of eight patients with linear 'discoid' le
sions, the age at onset was under 14 years; no patient has progressed
to systemic lupus erythematosus. Patients with 'linear' DLE may compos
e a certain clinical subset, We propose the term 'linear cutaneous lup
us erythematosus' which may be more suitable for the linear lesions of
DLE.