This study reports on the findings of longitudinal follow-up of visual
function in a 12-year-old girl affected by congenital right hemihydra
nencephaly. This extremely rare unilateral brain malformation allowed
the authors to gather new information on neuronal plasticity and funct
ional compensations of the visual system across a period of 10 years.
An extension of the preserved right visual hemifields above the middle
line and strategical eye or head positions developed to increase visu
al functions are discussed. In addition, ophthalmological and orthopti
cal findings, as well as the development of monocular grating and line
ar acuity, are described.