AORTIC-VALVE SURGERY IN OSTEOGENESIS IMPERFECTA - REPORT OF 2 CASES AND REVIEW OF THE LITERATURE

Authors
ZEGDI R DATTELLIS N FORNES P FUZELLIER EF CARTEAUX JP FABIANI JN CARPENTIER A
Citation
R. Zegdi et al., AORTIC-VALVE SURGERY IN OSTEOGENESIS IMPERFECTA - REPORT OF 2 CASES AND REVIEW OF THE LITERATURE, Journal of heart valve disease, 7(5), 1998, pp. 510-514
Citations number
30
Categorie Soggetti
Cardiac & Cardiovascular System
Journal title
Journal of heart valve disease → ACNP
ISSN journal
09668519
Volume
7
Issue
5
Year of publication
1998
Pages
510 - 514
Database
ISI
SICI code
0966-8519(1998)7:5<510:ASIOI->2.0.ZU;2-D
Abstract
Aortic insufficiency is a well known but uncommon valvular dysfunction in patients with osteogenesis imperfecta. In such cases, aortic valve surgery has rarely been performed, and carries a high risk of periope rative complications. We report two patients with osteogenesis imperfe cta, who underwent elective successful aortic valve replacement. The s urgical problems encountered in this connective tissue disorder are al so reviewed.