NUTRITION AND CYSTIC-FIBROSIS

Cystic fibrosis is commonly associated with energy deficiency in child ren and adults. Chronic undernutrition will lead to failure to thrive, wasting, and stunting of linear growth; nutrition and survival ate in timately related in cystic fibrosis. These problems can simply be cons idered as energy imbalance, and management centers on restoration of e nergy balance, Specific nutrient deficiencies, such as fat soluble vit amins, are common in cystic fibrosis. Recent work has highlighted prob lems with bone density and also the prevalence of vitamin K deficiency . Management of nutritional problems can be complex, and injudicious t reatment can further worsen the situation, as the relationship between high daily doses of pancreatic enzymes and the development of fibrosi ng colonopathy illustrates. (C) Elsevier Science Inc. 1998.