Glomerulocystic disease (GCD) is a very rare condition. Only two previ
ous reports have linked this condition with hepatoblastoma. We report
a neonate with US evidence of grossly enlarged echogenic kidneys and f
eatures typical of hepatic fibrosis, complicated by the presence of a
hepatoblastoma. The report discusses the differential diagnosis and hi
ghlights GCD as one cause of large, bright kidneys on US. It also adds
further evidence to the suggested association between GCD and hepatob
lastoma.