ADAPTIVE AND MALADAPTIVE BEHAVIOR IN CHILDREN WITH CRI-DU-CHAT SYNDROME

Twenty children with cri-du-chat syndrome were assessed on the Vinelan d Adaptive Behavioural Scales. Strengths within rather than between th e adaptive domains were identified with posthoc analyses revealing the main differences to lie within the domains of Communication and Daily -living Skills. In the former domain, Receptive Skills were significan tly more developed than Expressive and Written skills; and in the latt er domain, Personal skills were significantly more developed than Comm unity-based Skills. The core behavioural problems were Hyperactivity, poor Concentration span and Impulsivity. The implications of the prese nt findings are discussed with reference to the development of effecti ve remedial programmes that take into account the strengths and weakne sses in the adaptive and maladaptive profile of children with cri-du-c hat syndrome.