CONGENITAL COMPLETE ATRIOVENTRICULAR-BLOCK IN AN INFANT WITH LONG QT SYNDROME

A three months old patient with congenital complete atrioventricular b lock and prolonged QT interval syndrome is presented. Before admission she had had two syncopal attacks. During hospitalization she had an e pisode of torsade de pointes which was followed by ventricular fibrill ation. After a successful cardiopulmonary resuscitation, a permanent e picardial ventricular pacemaker was implanted and she was discharged o n propranolol therapy. She is now free of symptoms and doing well, 16 months after discharge.