Stapes surgery for correction of conductive hearing loss in adults with oto
sclerosis is a well-established procedure. Its effectiveness in children, h
owever, has received less scrutiny in the literature. Previous studies from
our and other institutions demonstrated similar results in children and ad
ults. Between 1980 and 1994 stapedectomies were done on 95 ears of 81 patie
nts younger than 18 years (83 primary and 12 revisions). Data regarding age
of onset, family history, associated anomalies, surgical findings, techniq
ue, hearing results, and complications were reviewed. Two groups were ident
ified: congenital stapedial fixation and juvenile otosclerosis. Patients wi
th congenital stapedial fixation had an earlier onset of hearing loss (3 vs
10 years, P < 0.001), a greater incidence of abnormalities of the malleus
and incus (25% vs 3%, P < 0.001), and a slightly greater preoperative air-b
one gap (35.2 +/- 12.9 vs 27.8 +/- 8.9, P = 0.002). Patients with otosclero
sis had a greater frequency of a positive family history of deafness (53% v
s 10%, P < 0.001). Overall, 79% of primary cases and 89% of revision cases
had an improvement in hearing, with mean postoperative air-bone gaps of 15
dB and 22 dB, respectively. The gap did not widen significantly during the
entire length of follow-up (mean 72 months). In primary cases, 59.1% obtain
ed a postoperative air-bone gap of 10 dB or less, Eighty-two percent of chi
ldren operated on for otosclerosis obtained excellent results (postoperativ
e air-bone gap less than or equal to 10 dB), compared with only 44% of chil
dren with congenital stapedial ankylosis (P = 0.02). In revision surgery, 2
9% of children obtained excellent results. Poorer results in both cases of
congenital stapedial fixation and revision stapedectomy appear to be relate
d to the greater incidence of associated anomalies of the malleus and incus
. Indications, technique, complications, and considerations pertinent to ch
ildhood stapedectomy are discussed.