RECENT FINDINGS IN CLASSIFICATION OF OSTEOGENESIS IMPERFECTA BY MEANSOF EXISTING DENTAL SYMPTOMS

The findings are based on a clinical investigation conducted on forty- nine patients suffering from osteogenesis imperfecta (OI), as well as on a questionnaire study in which 117 osteogenesis imperfecta-affected persons or their parents were involved. The survey established pathol ogical tooth discolorations as well as tooth abrasions. Dentinogenesis imperfecta (DI) was more frequently found in primary teeth than in pe rmanent teeth. There were no gender-specific differences. Radiological abnormalities were found in both, abraded and/or discolored teeth, as well as in clinically normal appearing teeth. In most cases there wer e club-shaped extensions of the pulp chambers and obliterations of the root canals. The probability that dentinogenesis imperfecta occurs as an accompanying symptom of osteogenesis imperfecta was not dependent on the degree of skeletal severity. The self-assignment according to A and B forms of osteogenesis imperfecta types I and IV in accordance w ith the presence/absence of dental symptoms was contradictory, since t he literature was based on varying classifications.