APERT SYNDROME

This paper discusses 33 cases of Apert's syndrome which were treated i n the Australian Craniofacial unit at the adelaide Children's Hospital . The main features were discussed. We found that mild ventricular dil atation is common in Apert's syndrome but without associated raised in tracranial pressure. Severe ventricular dilatation was seen in only on e case. No shunt procedures were performed. We also studied the change s in the ventricular size after transcranial corrective procedures. Th ere was no significant change in the ventricular size, the increase in the skull volume was compensated by expansion of the brain tissue and to some extent by increase in the subarachnoid space. Two cases with unusual features are also described.