There has been disagreement regarding surgical intervention in treatin
g pediatric patients with Chiari I malformation with headache as sole
complaint. Therefore, we retrospectively reviewed our experience over
a 6-year period, with patients less than 5 years of age (mean = 34.8 m
onths) with radiographically confirmed Chiari I malformation. We ident
ified 7 patients who presented with headaches as their only complaint.
The headaches varied in location and severity. All patients were trea
ted with posterior fossa decompression and syringosubarachnoid shunt w
hen indicated. At follow-up, all patients were noted to have rapid cli
nical improvement (mean = 11.6 weeks) and remain asymptomatic. Our dat
a suggest that patients less than 5 years of age with Chiari I malform
ation benefit from surgical decompression when presenting with a chief
complaint of headache.