Purpose To describe the significance of macular changes to visual outc
ome in benign intracranial hypertension (BIH). Method The clinical and
photographic records of 24 patients with Bill who required optic nerv
e sheath fenestration were analysed. Results Macular changes were foun
d in 21 of 48 (44%) eyes. These were: choroidal folds 9; circumferenti
al lines (Paton's lines) 4; nerve fibre layer haemorrhage 3; macular s
tars 5; macular oedema 6; retinal pigment epithelial changes 4;subreti
nal haemorrhage leading to a macular scar 1. Significant visual loss a
ttributable to the macular changes was found in 5 eyes in the short te
rm and 3 in the long term. The 2 eyes that improved had macular stars,
Of the 3 eyes that did not improve, 2 eyes had retinal pigment epithe
lial changes and 1 a large subretinal haemorrhage that led to a macula
r scar. These 3 cases had long-standing BIH. Conclusions The majority
of macular changes resolve and do not add to visual loss from optic ne
rve damage. Patients with marked macular oedema are at most risk of pe
rmanent visual loss and should be considered for early treatment such
as optic nerve sheath fenestration.