GANGLIONEUROBLASTOMA IN AN ADULT

Citation
P. Rousseau et al., GANGLIONEUROBLASTOMA IN AN ADULT, La Presse medicale, 27(33), 1998, pp. 1677-1679
Citations number
17
Categorie Soggetti
Medicine, General & Internal
Journal title
ISSN journal
07554982
Volume
27
Issue
33
Year of publication
1998
Pages
1677 - 1679
Database
ISI
SICI code
0755-4982(1998)27:33<1677:GIAA>2.0.ZU;2-1
Abstract
BACKGROUND: Ganglioneuroblastoma is commonly observed in children but rarely in adults. Therapy and prognosis are not well defined in adults . CASE REPORT: We report the case of a female adult who developed a ga nglioneuroblastoma of the left adrenal gland with liver metastasis. Su rgical treatment combined with radio and chemotherapy led to complete remission. DISCUSSION: The outcome in our patient and data reported in the literature suggest that a multidisciplinary approach is necessary and that initial surgical resection should be performed whenever poss ible. Adjuvant radiotherapy or chemotherapy have been shown to be some what effective in children but their true impact in adults remains to be ascertained. Follow-up after resection should include physical exam ination, assay of adrenal derivatives in plasma and urine and imaging.