NEOPLASM OF ENDOLYMPHATIC SAC ORIGIN - CLINICAL, RADIOLOGICAL AND PATHOLOGICAL FEATURES

This paper reports on a 55-year-old female who had undergone middle ea r surgery 12 years previously and was admitted with a 6-months history of unilateral hearing loss and facial weakness. MRI and CT demonstrat ed a space-occupying lesion arising from the temporal bone and extendi ng into the posterior fossa. Treatment consisted in complete tumour re moval. Temporal and mastoid bone destruction associated with typical h istological features led to the diagnosis of neoplasm of endolymphatic sac origin. Clinical, histological, radiological and intra-operative features of these rare tumours are described and discussed. The pertin ent literature is reviewed.