A nephrotic syndrome with focal sclerosis associated with Kimura's dis
ease is reported in a young asiatic man. The nephrotic syndrom started
three years prior to the usual skin tumors and lymph nodes involvemen
t. Epidemiological, clinical and nosological characteristics of Kimura
's disease are discussed. Renal manifestations are the only visceral l
ocalisations of the disease. Thirteen Kimura's disease associated with
documented nephrotic syndromes have been reported in german-english l
iterature. They display a wide variety of histologic patterns. Their c
linical course do not differ from the primary form of nephrotic syndro
m with identical histology.