LINEAR AND WHORLED NEVOID HYPERMELANOSIS - REPORT OF 2 CASES

Case reports. - Two cases of linear and whorled nevoid hypermelanosis are reported. Cutaneous lesions (hyperpigmented macules along Blaschko 's lines) appeared gradually after birth. Neurologic anomalies were de tected in both cases (symptomatic in one, only cerebral MRI anomalies in the other). Conclusion, - This sporadic condition, probably caused by somatic mosaicism, must be differentiated from incontinentia pigmen ti, Mac Cune-Albright disease and chimerism. Its situation among the B laschko linear pigmentary anomalies (hypomelanosis of to) is discussed . (C) 1998 Elsevier, Paris.